The first is the
collection and amplification of the sound, using the external ear, ear
canal, eardrum and the ear bones in the
middle ear. Disease in this
area of the ear will cause a "Conductive Loss" or loss of sound
loudness. Surgery will often restore the hearing to near normal levels
and if the patient is unable to undergo surgery a hearing aid will greatly benefit
the patient. Even an simple auditory amplifier which costs under $50
can return the hearing to normal. This type of hearing loss is most
commonly found in children and presents as an ear infection or ear
fluid. Examples of Conductive Hearing Losses:
Eustachian tube
dysfunction - Negative pressure in the ear can cause a mild hearing
loss, but can also lead to more serious conditions such as ear fluid or
a cholesteatoma. Treatment of negative pressure is by popping the
ears and observation by your doctor.
Search PubMed for Cholesteatoma
The second is the
processing of the sound by the cochlea and converting the sound into nerve
impulses and transmitting them to the brain via the auditory nerve.
The processing of the sound is very complex, parts of the sound are actually
recreated by the
inner ear
and can be heard by use of a microphone.
This process is the basis for otoacoustic emission testing in
children. Hearing losses involving this process are called
sensorineural. Sensory for losses involving the cochlea and neural for
losses involving the auditory nerve. Sensorineural hearing losses are
most common in the adult. Unfortunately, there is no cure for these
losses but the most common type, noise-induced hearing loss, are
preventable. If the loss is determined to be neuronal in type, a
central lesion, such as a brain tumor, needs to be sought for.
Hearing
aids will help patients with this type of hearing loss, but usually do
not restore the hearing to normal. Examples of sensorineural hearing loss:
Sometimes a
hearing loss comes on quickly, without warning and for no know reason.
These hearing losses are called a " Sudden Sensorineural Hearing Loss ".
All other causes, such as an acoustic neuroma, should be excluded before
this diagnosis is made. Steroids, when given early, have been show to help some patients.
View Article
View Article. The use of
antiviral agents are controversial with some authors having shown them to be ineffective.
View Article Physicians
have also
advocated the use of agents to increase blood flow, such as plasma
expanders and vasodilators but these medications have not been proven to be
effective.
View ArticleTreatment should also include strict limits on heavy lifting
and straining.
An
acoustic neuroma is a slowly growing benign tumor located on the
auditory nerve. Although benign, it can be fatal if left
untreated. Up to 10% of autopsies on normal patients have been
reported to contain acoustic neuromas. Thus, some small neuromas
in older patients are followed to see if they will grow.
Patients with a hearing loss
that is worse in one ear than the other should be considered at risk for
this disease. Most should undergo a brain stem auditory evoked
response or MRI scan.
The patient shown in the right
MRI scans, had only a 20 dB loss at 2000 Hz and 4000 Hz. He had
100% discrimination (understanding of words) which is not characteristic
of a neuronal hearing loss. The neuroma showed significant growth
over a 3 year period. It was removed using a sub-occipital
approach.
MRI Scan
8/30/1997
MRI Scan
8/28/2000
This patient is a 35 yr old female
with a condition called neurofibromatosis. Shown in her initial
MRI scan are bilateral acoustic (ear) and orbit (eye) lesions. She
presented with a unilateral hearing loss with poor discrimination.
To learn more about neurofibromatosis, go to the National Neurofibromatosis
Foundation Website:
http://neurofibromatosis.org/
Page last updated
01/19/2008,
Page Views Since 12/15/2003
Copyright 2001 Kevin Kavanagh All rights reserved
Google Ads are a
sponsor of ENT USA Website. ENT USA, Cumberland Otolaryngology
or Dr Kevin Kavanagh, MD do not endorse or are responsible for the
content or claims made
in the Advertisements.